Which statement best describes Brugada syndrome?

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Brugada syndrome is a congenital sodium channelopathy that presents with ST-segment elevation in the right precordial leads, especially V1 through V3, with a coved-type pattern that often resembles a right bundle branch block. This Type 1 Brugada pattern arises from reduced inward sodium current, frequently due to SCN5A mutations, creating an arrhythmogenic substrate in the right ventricular outflow tract and increasing the risk of ventricular fibrillation and sudden death. The hallmark is about 2 mm or more of ST elevation with a downward, coved morphology into a negative or biphasic T wave. The other electrolyte-related conditions produce different ECG patterns: hyperkalemia shows tall T waves with QRS widening; hypocalcemia prolongs the QT interval; hypokalemia typically presents with prominent U waves. In short, the description of Brugada as a congenital sodium channelopathy with a coved ST-segment elevation in V1–V3 (often with an RBBB-like appearance) best describes the syndrome.